Mauriac syndrome is an uncommon syndrome described. Mauriac syndrome is a rare complication of type 1 diabetes characterized by extreme liver enlargement due to glycogen deposition, along with growth failure and delayed puberty. Pdf on may 1, 2012, prem p patidar and others published a rare case of mauriac syndrome find. Type 1 diabetes mellitus dm1 is one of the most important pediatric endocrinology diseases. Find, read and cite all the research you need on researchgate. Type 1 diabetes mellitus is a chronic metabolic disease whith increasing incidence. Mauriac syndrome, uncommon presentation of a common disease. Mauriac syndrome ms is a glycogenic hepatopathy, initially described in 1930, characterized by growth failure, delayed puberty, cushingoid appearance, hepatomegaly with abnormal liver enzymes. Hg is one of the components of mauriac syndrome ms, initially. Mauriac syndrome is an uncommon complication of poorlycontrolled type 1 diabetes mellitus t1dm reported. Mauriac syndrome, diabetes mellitus tipo 1, undernutrition, malnutrition, dwarfism, hypogonadism.
Mauriac syndrome, first described in 1930, is typically diagnosed in young patients with poorly controlled type 1 diabetes mellitus and growth. An insulindependent diabetic was diagnosed at the age of 7 years. It occurs in some children and adolescents with type 1 diabetes irrespective of their glycemic control. Claudia constantino 1, joao farela neves 1, raquel marta 1, gabriela pereira 1, deolinda barata 1, lurdes lopes 2. Cuidados intensivos, hospital dona estefania, chlisboa central.
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